Pediatric Gastroenterology, Hepatology & Nutrition

The Korean Society of Pediatric Gastroenterology, Hepatology and Nutrition (대한소아소화기영양학회)
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A Case of Mesenchymal Hamartoma Associated with Biliary Atresia

담도 폐쇄증 환아에서 우연히 발견된 간엽 과오종 1례

  • Choi, Kyung-Dan (Department of Pediatrics, Seoul National University College of Medicine) ;
  • Seo, Jeong-Kee (Department of Pediatrics, Seoul National University College of Medicine) ;
  • Shin, Eon-Woo (Department of Pediatrics, Seoul National University College of Medicine) ;
  • Ko, Jae-Sung (Department of Pediatrics, Seoul National University College of Medicine) ;
  • Kim, Woo-Sun (Department of Radiology, Seoul National University College of Medicine) ;
  • Park, Young-Su (Department of Pathology, Seoul National University College of Medicine) ;
  • Kang, Kyung-Hoon (Department of Pathology, Seoul National University College of Medicine) ;
  • Chi, Je-Geun (Department of Pathology, Seoul National University College of Medicine)
  • 최경단 (서울대학교 의과대학 소아과학교실) ;
  • 서정기 (서울대학교 의과대학 소아과학교실) ;
  • 신언우 (서울대학교 의과대학 소아과학교실) ;
  • 고재성 (서울대학교 의과대학 소아과학교실) ;
  • 김우선 (서울대학교 의과대학 진단방사선과학교실) ;
  • 박영수 (서울대학교 의과대학 병리학교실) ;
  • 강경훈 (서울대학교 의과대학 병리학교실) ;
  • 지제근 (서울대학교 의과대학 병리학교실)
  • Received : 2001.02.28
  • Accepted : 2001.03.24
  • Published : 2001.04.30
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Abstract

Mesenchymal hamartoma is an uncommon benign tumor usually found in childhood, especially during the first two years of life. The tumor consists of a solid component and multiple cyst. Without treatment, these lesions can grow to an enormous size. We experienced a case of mesenchymal hamartoma which was found incidentally, in a 8 month old girl who had ascending cholangitis after Kasai operation due to biliary atresia. On abdominal ultrasonography and CT, there was a well-defined homogeneous small echogenic mass in the right lobe of the liver with cirrhosis. Five months later, she underwent liver transplantation. Gross picture of the resected liver showed a dark greenish pigmented solid mass in the right lobe of the cirrhotic liver. Microscopic findings showed reactive mesenchyma and epithelial overgrowth.

소아에서 간의 간엽 과오종은 주로 복부팽만을 주소로 내원하여 대부분 2세 이내에 발견되며, 비교적 크기가 큰 낭종의 소견을 보이는 것으로 알려져 있다. 저자들은 담도 폐쇄증으로 Kasai 수술받은 8개월 여아에서 복부 초음파 검사상 작은 기질성 종괴를 우연히 발견하여 병리학적으로 확진된 간엽과오종 1례를 보고하는 바이다.

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