Myositis Ossificans Progressiva localized on hands and feet with slow progression - One case report -

수족부에 국한되어 완만한 임상경과를 보이는 진행성 골화성 근염 - 1예 보고 -

  • Kim, Jae-Hwa (Department of Orthopaedic Surgery, Pundang CHA College of Medicine) ;
  • Cho, Duck-Yun (Department of Orthopaedic Surgery, Pundang CHA College of Medicine) ;
  • Yoon, Hyung-Ku (Department of Orthopaedic Surgery, Pundang CHA College of Medicine) ;
  • Han, Soo-Hong (Department of Orthopaedic Surgery, Pundang CHA College of Medicine) ;
  • Kim, Dong-Jun (Department of Orthopaedic Surgery, Pundang CHA College of Medicine)
  • 김재화 (포천중문 의과대학 분당 차병원 정형외과학교실) ;
  • 조덕연 (포천중문 의과대학 분당 차병원 정형외과학교실) ;
  • 윤형구 (포천중문 의과대학 분당 차병원 정형외과학교실) ;
  • 한수홍 (포천중문 의과대학 분당 차병원 정형외과학교실) ;
  • 김동준 (포천중문 의과대학 분당 차병원 정형외과학교실)
  • Published : 2002.12.01

Abstract

Myositis ossificans progressiva, otherwise called fibrodysplasia ossificans progressiva is a rare hereditary disease of unknown etiology, which is characterized by progressive ectopic ossification in connective tissues of the muscles, tendons, fascia and aponeurosis. We report a case of myositis ossificans progressiva confined to hands and feet, which has an unusual clinical feature with slow progression.

Keywords