Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Congenital Left Main Coronary Artery Atresia

선천성 좌주관상동맥 폐쇄증

  • Min Sun-Kyung (Department of Thoracic and Cardiovascular Surgery, Samsung Medical Center, Sungkyunkwan University School of Medicine) ;
  • Choi Se-Hoon (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine) ;
  • Jang Woo-Sung (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine) ;
  • Lee Jae-Hang (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine) ;
  • Kim Chang-Young (Department of Thoracic and Cardiovascular Surgery, Ilsan Paik Hospital, Inje University College of Medicine) ;
  • Kim Woong-Han (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine)
  • 민선경 (성균관대학교 의과대학 삼성서울병원 흉부외과) ;
  • 최세훈 (서울대학교 의과대학 서울대학교병원 흉부외과) ;
  • 장우성 (서울대학교 의과대학 서울대학교병원 흉부외과) ;
  • 이재항 (서울대학교 의과대학 서울대학교병원 흉부외과) ;
  • 김창영 (인제대학교 의과대학 일산백병원 흉부외과) ;
  • 김웅한 (서울대학교 의과대학 서울대학교병원 흉부외과)
  • Published : 2006.10.01
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Abstract

Left main coronary artery atresia is a very rare congenital coronary anomaly with blind end of left main trunk. The clinical symptoms as syncope, failure to thrive, and myocardial infarction are presented and surgical treatments are required in most cases. We report a case of a 14-months-old girl with left main coronary artery atresia and excel-lent surgical result of 1 year follow-up after coronary artery bypass with left internal thoracic artery.

좌주관상동맥 폐쇄증은 매우 드문 선천성 관상동맥 기형의 하나로 좌주관상동맥의 근위부가 단절되어 있어서 대부분의 경우 실신이나 성장지연, 심근경색 등의 증상을 나타내며 수술적 치료를 요한다. 호흡곤란을 주소로 내원한 생후 14개월 여아에서 좌주관상동맥 폐쇄증이 진단되어 내흉동맥을 이용한 관상동맥 우회술 시행 후 1년 이상의 추적관찰로 좋은 결과를 확인할 수 있었기에 보고하는 바이다.

Keywords

References

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