Retroperitoneal Pulmonary Sequestration in a Neonate - A case report -

신생아에서 발견된 후복막강 폐격리증 - 1예 보고 -

  • Lee, Hyung-Chae (Department of Thoracic and Cardiovascular Surgery, Pusan Paik Hospital, College of Medicine, Inje University) ;
  • Cho, Kwang-Hyun (Department of Thoracic and Cardiovascular Surgery, Pusan Paik Hospital, College of Medicine, Inje University) ;
  • Choi, Kwang-Ho (Department of Thoracic and Cardiovascular Surgery, Pusan Paik Hospital, College of Medicine, Inje University) ;
  • Yoon, Young-Chul (Department of Thoracic and Cardiovascular Surgery, Pusan Paik Hospital, College of Medicine, Inje University) ;
  • Lee, Yang-Haeng (Department of Thoracic and Cardiovascular Surgery, Pusan Paik Hospital, College of Medicine, Inje University) ;
  • Hwang, Youn-Ho (Department of Thoracic and Cardiovascular Surgery, Pusan Paik Hospital, College of Medicine, Inje University)
  • 이형채 (인제대학교 의과대학 부산백병원 흉부외과학교실) ;
  • 조광현 (인제대학교 의과대학 부산백병원 흉부외과학교실) ;
  • 최광호 (인제대학교 의과대학 부산백병원 흉부외과학교실) ;
  • 윤영철 (인제대학교 의과대학 부산백병원 흉부외과학교실) ;
  • 이양행 (인제대학교 의과대학 부산백병원 흉부외과학교실) ;
  • 황윤호 (인제대학교 의과대학 부산백병원 흉부외과학교실)
  • Published : 2009.06.05

Abstract

Retroperitoneal pulmonary sequestration is an extremely rare congenital malformation. It is more frequently diagnosed in the antenatal period due to routine ultrasonic examinations that are conducted for a fetus or during the first 6 months of life, although retroperitoneal pulmonary sequestration is incidentally discovered in adults on rare occasions. Because the location and radiological findings of retroperitoneal pulmonary sequestration are very similar to those of another retroperitoneal masses, retroperitoneal pulmonary sequestration, although they are very rare, should be included in the differential diagnosis of a retroperitoneal suprarenal mass. Although fine needle aspiration may be considered as an aid for making the preoperative diagnosis, surgery remains the treatment of choice for symptomatic lesions and this surgery is associated with excellent results and a good prognosis.

후복막강 폐격리증은 극히 드문 질환으로 보통은 임신 6개월경에 시행하는 태아 초음파로 발견되며 드물지만 성인에서 우연히 발견된다. 후복막강 폐격리증은 그 위치와 방사선학적인 소견이 신경아세포종 등의 다른 후복막강 종괴와 아주 유사하기 때문에 그 발생 빈도가 극히 드물더라도 후복막강 종괴가 의심될 때 감별을 요한다. 세침 흡입 검사가 수술 전 진단에 도움이 된다고 하지만, 수술적 제거가 환자의 예후나 경과를 생각 했을때 좋은 치료 방법이라고 생각된다.

Keywords

References

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