Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Spontaneous Hemothorax in a Patient with Type IV Ehlers-Danlos Syndrome - A case report -

제4형 Ehlers-Danlos 증후군 환자에서 발생한 자발성 혈흉 - 1예 보고 -

  • Han, Kook-Nam (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine) ;
  • Kim, Young-Tae (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine) ;
  • Nam, Jin-Hae (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine) ;
  • Choi, Jin-Ho (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine) ;
  • Kang, Chang-Hyun (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine) ;
  • Kim, Joo-Hyun (Department of Thoracic and Cardiovascular Surgery, Seoul National University Hospital, Seoul National University College of Medicine)
  • 한국남 (서울대학교병원 흉부외과, 서울대학교 의과대학 흉부외과학교실) ;
  • 김영태 (서울대학교병원 흉부외과, 서울대학교 의과대학 흉부외과학교실) ;
  • 남진혜 (서울대학교병원 흉부외과, 서울대학교 의과대학 흉부외과학교실) ;
  • 최진호 (서울대학교병원 흉부외과, 서울대학교 의과대학 흉부외과학교실) ;
  • 강창현 (서울대학교병원 흉부외과, 서울대학교 의과대학 흉부외과학교실) ;
  • 김주현 (서울대학교병원 흉부외과, 서울대학교 의과대학 흉부외과학교실)
  • Received : 2009.11.06
  • Accepted : 2010.01.27
  • Published : 2010.06.05
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Abstract

We successfully performed bleeding control using roll-gauze packing in a patient with Type IV Ehlers-Danlos syndrome and this patient was suffering from spontaneous hemothorax. Thoracotomy for controlling ongoing bleeding in a patient with Type IV Ehlers-Danlos syndrome should be performed as a last resort after due consideration.

제 4형 Ehlers-Danlos 증후군 혈관 침범형 환자에서 발생한 자발적 혈흉을 개흉술 후 거즈를 충전 압박하여 성공적으로 지혈하였다. 지혈이 어려울 것으로 예상되는 환자에서 지혈 목적의 개흉 수술은 최후의 방법으로 신중히 고려되어야 할 것으로 보인다.

Keywords

References

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