Annals of Clinical Neurophysiology

The Korean Society of Clinical Neurophysiology (대한임상신경생리학회)
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Recurrent Myelopathy in a Patient with Klippel-Trenaunay Syndrome

클리펠-트레노네이증후군 환자에서 발생한 재발척수병

  • Kim, Yue Kyung (Department of Neurology, Ajou University School of Medicine) ;
  • Eom, Young In (Department of Neurology, Ajou University School of Medicine) ;
  • Joo, In Soo (Department of Neurology, Ajou University School of Medicine)
  • 김유경 (아주대학교 의과대학 신경과학교실) ;
  • 엄영인 (아주대학교 의과대학 신경과학교실) ;
  • 주인수 (아주대학교 의과대학 신경과학교실)
  • Received : 2014.11.04
  • Accepted : 2015.07.08
  • Published : 2015.12.31
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Abstract

Klippel-Trenaunay syndrome (KTS) is a rare congenital malformation syndrome involving blood and lymph vessels, which is characterized by triad of cutaneous hemangioma, venous varicosities, and overgrowth of the affected limbs. Because vascular malformation in KTS can be located anywhere except the face and brain, the clinical presentation could be extremely variable. But there are only rare case reports that KTS is associated with spinal cord lesion. We report a case of recurrent myelopathy in a patient with KTS.

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References

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