Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Bentall Operation in a Patient with a Unicommissural Unicuspid Aortic Valve

  • Park, Sung Joon (Department of Thoracic and Cardiovascular Surgery, Inje University Sanggye Paik Hospital, Inje University College of Medicine) ;
  • Lee, Jae Hoon (Department of Thoracic and Cardiovascular Surgery, Inje University Sanggye Paik Hospital, Inje University College of Medicine) ;
  • Chung, Eui Suk (Department of Thoracic and Cardiovascular Surgery, Inje University Sanggye Paik Hospital, Inje University College of Medicine)
  • Received : 2019.03.20
  • Accepted : 2019.07.29
  • Published : 2019.10.05
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Abstract

A unicuspid aortic valve is a rare congenital malformation that frequently presents with valvular dysfunction and dilatation or aortic aneurysm, requiring combined aortic valve surgery and aortic repair. Some patients show severe valve calcification extending into the interventricular septum, possibly resulting in damage to the conduction system during debridement for valve replacement. We present a rare case of severe aortic stenosis with a unicommissural unicuspid aortic valve diagnosed by preoperative transesophageal echocardiography in a 36-year-old man. After composite graft replacement of the aortic valve, aortic root, and ascending aorta, a permanent pacemaker was placed because of postoperative complete heart block.

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References

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Cited by

  1. Unicuspid aortic valve: Case series and review vol.37, pp.12, 2020, https://doi.org/10.1111/echo.14885