Journal of Chest Surgery

The Korean Society for Thoracic and Cardiovascular Surgery (대한심장혈관흉부외과학회)
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Truncus Arteriosus associated with Interrupted Aortic Arch

대동맥궁 단절을 동반한 동맥간

  • Kim Kwan Chang (Department of Thoracic and Cardiovascular Surgery Seoul National University Children's Hospital, Seoul National University College of Medicine) ;
  • Choi Sae Hoon (Department of Thoracic and Cardiovascular Surgery Seoul National University Children's Hospital, Seoul National University College of Medicine) ;
  • Jang Woo Sung (Department of Thoracic and Cardiovascular Surgery Seoul National University Children's Hospital, Seoul National University College of Medicine) ;
  • Yeo In Gwon (Department of Thoracic and Cardiovascular Surgery Seoul National University Children's Hospital, Seoul National University College of Medicine) ;
  • Kim Woong-Han (Department of Thoracic and Cardiovascular Surgery Seoul National University Children's Hospital, Seoul National University College of Medicine)
  • 김관창 (서울대학교 어린이병원 흉부외과, 서울대학교 의과대학 흉부외과학교실) ;
  • 최세훈 (서울대학교 어린이병원 흉부외과, 서울대학교 의과대학 흉부외과학교실) ;
  • 장우성 (서울대학교 어린이병원 흉부외과, 서울대학교 의과대학 흉부외과학교실) ;
  • 여인권 (서울대학교 어린이병원 흉부외과, 서울대학교 의과대학 흉부외과학교실) ;
  • 김웅한 (서울대학교 어린이병원 흉부외과, 서울대학교 의과대학 흉부외과학교실)
  • Published : 2005.12.01
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Abstract

A 85-day-old infant was successfully operated on for truncus arteriosus (type I) with interrupted aortic arch (type A) using one-stage anterior approach without circulatory arrest. Aortic arch was reconstructed by direct anastomosis of ascending aorta and descending aorta with regional perfusion and continuity of right ventricle to pulmonary artery was established with $Shelhigh^{circledR}$ pulmonic conduit. The patient experienced left bronchus compression by descending aorta immediately postoperatively, which was improved with positional change and physiotherapy. The patient had reoperation due to stenosis of valved conduit at 13 months later. The patient is currently well under follow-up of 14 months from initial repair.

생후 85일 된 대동맥궁 단절이 동반된 총동맥간 환자에서 완전순환정지 없이 1차 완전 교정술을 성공적으로 시행하였다. 대동맥 단절 교정은 국소순환하에 상행 및 하행대동맥을 문합하였고 우심실유출로 재건은 Shelhigh 판막도관을 이용하였다. 술 후 혈관에 의해 일시적으로 좌측 기관지가 눌리는 합병증이 발생하였으나 자세변화와 흉부물리치료로 호전되었다. 술 후 13개월 뒤에 판막도관의 협착으로 우심실 유출로에 대한 재수술이 필요했으며 환아는 현재 건강한 상태로 첫 교정술 후 14개월째 외래 추적중이다.

Keywords

References

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