심실 중격 결손과 대동맥 판 협착을 가진 대동맥 궁 단절의 일차 완전 교정술 -1예 보고-

One-stage Repair of Interrupted Aortic Arch with Ventricular Septal Defect and Valvular Aortic Stenosis - A case report-

  • 조준용 (경북대학교병원 흉부외과) ;
  • 정영균 (경북대학교병원 흉부외과) ;
  • 이종태 (경북대학교병원 흉부외과) ;
  • 김규태 (경북대학교병원 흉부외과) ;
  • 장봉현 (경북대학교병원 흉부외과)
  • Cho, Joon-Yong (Department of Thoracic and Cardiovascular Surgery, Kyungpook National University Hospital) ;
  • Jeong, Young-Kyun (Department of Thoracic and Cardiovascular Surgery, Kyungpook National University Hospital) ;
  • Lee, Jong-Tae (Department of Thoracic and Cardiovascular Surgery, Kyungpook National University Hospital) ;
  • Kim, Kyu-Tae (Department of Thoracic and Cardiovascular Surgery, Kyungpook National University Hospital) ;
  • Chang, Bong-Hyun (Department of Thoracic and Cardiovascular Surgery, Kyungpook National University Hospital)
  • 발행 : 2005.12.01

초록

생후 19일 된 남아가 안면 청색증과 과호흡을 주소로 내원하였다. 심 초음파 소견 상 B형의 대동맥 궁 단절과 후방 부정열형의 심실 중격 결손, 대동맥 판 협착을 보였다. 수술은 양심실 교정을 시행하였으며, 대동맥 판과 폐동맥 판 모두를 좌심실 유출로로 이용하고 신 대동맥 궁을 재건하고 Goretex graft를 이용하여 우심실 유출로를 재건하는 새로운 방법으로 하였다. 술 후 좌심실 유출로와 우심실 유출로 모두 협착없이 잘 유지되었다.

A male neonate was referred to our hospital with facial cyanosis and tachypnea at 19 days of age. Two-dimensional echocardiography showed type B interrupted aortic arch, posterior malalignment ventricular septal defect and valvular aortic stenosis. A new surgical repair was done with biventricular repair and neo-aortic arch reconstruction. Left ventricular outflow track (LVOT) was consisted of aortic valve and pulmonic valve. Right ventricular outflow (RVOT) track was reconstructed with extracardiac conduit. Postoperative two-dimensional echocardiography showed no stenosis and turbulency flow on LVOT and RVOT.

키워드

참고문헌

  1. Van Praagh R, Bernhard WF, Rosenthal A, Parisi LF, Fyler DC. Interrupted aortic arch: Surgical treatment. Am J Caridiol 1971;27:200-11 https://doi.org/10.1016/0002-9149(71)90259-1
  2. Freedom RM, Bain HH, Esplugas E, Dische R, Rowe RD. Ventricular septal defect in interruption of aortic arch. Am J Cardiol 1977;39:572-82 https://doi.org/10.1016/S0002-9149(77)80168-9
  3. Bove EL, Minich LL, Pridjian AK, et al. The management of severe subaortic stenosis, ventricular septal defect, and aortic obstruction in the neonate. J Thorac Cardiovasc Surg 1993; 105:289-96
  4. Luciani GB, Ackerman RJ, Chang AC, Wells WJ, Starnes VA. One-stage repair of interrupted aortic arch, ventricular septal defect, and subaortic obstruction in the neonate: A novel approach. J Thorac Cardiovasc Surg 1996;111:348-58 https://doi.org/10.1016/S0022-5223(96)70444-0
  5. Yamagishi M, Fujiwara K, Yamada Y, Shuntoh K, Kitamura N. A new surgical technique for one-stage repair of interrupted aortic arch with valvular aortic stenosis. J Thorac Cardiovasc Surg 2001;122:392-3 https://doi.org/10.1067/mtc.2001.113748